Exam Preview for 17019: Update on Auditory Neuropathy September 9,

Update on Auditory Neuropathy

Please note: exam questions are subject to change.

1. Which of the following are not candidates for the site of lesion in ANSD: auditory nerve ganglion cells outer hair cells inner hair cells/auditory nerve synapse
2. The presence of a speech-evoked cortical auditory evoked potential in a child with ANSD would predict : some speech perception ability is never found in these cases normal hearing and processing ability misdiagnosis of auditory neuropathy
3. Which of the following measures is never expected to show normal results in a patient with ANSD: tympanometry ABR wave I TEOAE cochlear microphonic
4. Which of the following are not associated with ANSD: poor speech perception ability fluctuations in auditory sensitivity skin pigmentation disorders peripheral nerve disease
5. What change was made to the 2007 Joint Committee on Infant Hearing Statement that was relevant to ANSD? Audiologists should serve as infant screeners. ABR should be used to screen NICU infants. Both ABR and OAE in combination should be used for all infant screening. No changes were made.
6. Which of the following is most commonly seen in the history of a high risk infant with ANSD? Cleft palate Meningitis Hyperbilirubinemia Sepsis
7. Which of the following tests would be expected to show grossly abnormal results on patients with ANSD? air-bone gaps wide band reflectance real ear to coupler differences gap detection thresholds
8. What is the function of the protein Otoferlin? Aids in cross-membrane vesicle transmission Aids in rapid neural conduction Neurotransmitter Is necessary for the production of the cochlear microphonic
9. The cochlear microphonic is produced by outer hair cells inner hair cells neither A nor B Both A and B
10. Complete this sentence: Cochlear implants for children in ANSD should not be recommended because the auditory nerve is damaged in these patients. is generally a successful treatment for audiologically-appropriate candidates. will work in about 10% of children with ANSD and profound hearing loss. should be considered the first treatment of choice for these children.