Ask the Experts | Medical & Surgical | Large Vestibular Aqueduct Syndrome Large Vestibular Aqueduct Syndrome Dr. J. G. Neely May 24, 2004 Print Question Please discuss Large Vestibular Aqueduct Syndrome, including management and counseling. How often should hearing be monitored? Answer The enlarged vestibular aqueduct syndrome is operationally defined as a sudden and/or progressive sensorineural hearing loss in a patient with computed tomographic (CT) evidence of an enlarged vestibular aqueduct. Such enlargements may be seen in normally hearing individuals, but when seen in individuals with sensorineural hearing loss, the operational definition is partially met. If the hearing loss in these individuals progresses, the definition is fully met. Some of these patients become profoundly hearing impaired and require cochlear implantation.The exact mechanism of how this anatomic finding relates to the hearing loss is unknown; however, it might be associated with the well known and described Mondini malformation, which has a host of abnormalities of development within the vestibular and cochlear labyrinth. Abnormalities in chromosomal region 7q31 seem to be associated with this syndrome; the exact significance of this is yet to be determined. Treatment at this point is confined to hearing rehabilitation and educational structures that help hearing impaired individuals.I recommend reading: Miyamoto, Bradford, Wynne, and Kirk's article in the Laryngoscope, Volume 112, Part 7, July 2002, pages 1178-1182, titled "Cochlear Implantation With Large Vestibular Aqueduct Syndrome". Dr. J.G. Neely has been an academic otologic/neurotologic surgeon for 30 years. He started at Baylor College of Medicine in Houston, Texas, and then became Chairman, in the Department of Otorhinolaryngology, at the University of Oklahoma School of Medicine. Dr. Neely is the Director of Otology/Neurotology/Base of Skull Surgery, Department of Otolaryngology-Head and Neck Surgery, Washington University School of Medicine in St Louis, Missouri. Dr. J. G. Neely Director of Otology/Neurotology/Base of Skull Surgery Related Courses Presenter Bharti Katbamna, PhD, CCC-A Fetal Alcohol Syndrome: Effects on the Auditory System [Text/Transcript Course] Course: #17489 CEUs/Hours Offered: AAA/0.1 Intermediate; ACAud/0.1; AHIP/1.0; ASHA/0.1 Intermediate, Professional; BAA/1.0; CAA/1.0; CASLPA/1.0; IHS/1.0; Kansas DHE, LTS-S0035/1.0 Cost: Free to View This review describes the effects of prenatal alcohol exposure on the peripheral and central auditory nervous system and presents literature on possible pathogenesis and mechanisms of damage. Course Details Presenter Levi A. Reiter, PhD Ear Kissing (REKS): What You Don't Know Can Hurt You! [Recorded Course] Course: #14036 CEUs/Hours Offered: AAA/0.1 Intermediate; ACAud/0.1; AHIP/1.0; BAA/1.0; CAA/1.0; IHS/1.0; Kansas DHE, LTS-S0035/1.0 Cost: Free to View A kiss on the ear's aperture has been shown to result in sudden sensorineural hearing loss, tinnitus, and hyperacusis. This presentation explores the physiological mechanism underlying this ear-kiss syndrome. Course Details Presenters Don W. Worthington, PhD Bryan J. Layton, AuD Jocelyn Monroe, PT Rhoda Jenson, MS Vestibular Neuritis: Acute Clinical Picture [Text/Transcript Course] Course: #7612 CEUs/Hours Offered: AAA/0.1 Intermediate; ACAud/0.1; BAA/1.0; CAA/1.0; CASLPA/1.0; IHS/1.0; Kansas DHE, LTS-S0035/1.0 Cost: Free to View Editor's note 2/3/11: Dr. Worthington recently reviewed this article and indicated the information is still current and accurate, despite its original publishing date of 2006. -ED.The intent of this article is to present a case study of a 26-year-old male with Vestibular Neuritis who was initially seen during the acute stage of the disease. Vestibular function tests (performed by an audiologist) and vestibular rehabilitation (performed by a physical therapist) were performed on this young man within 3 days of symptom onset and follow-up testing and rehabilitation was performed at 2 weeks-, 5 weeks-, 10 weeks-, and 8 months post acute symptoms. Course Details Presenters Brad A. Stach, PhD Kenneth Bouchard, PhD Ashley Hallberg, AuD Adrianne Fazel, AuD Jacqueline Wiegers Kelsey Corcoran Audiology Grand Rounds at Henry Ford Hospital: Vestibular [Recorded Course] Course: #22061 CEUs/Hours Offered: AAA/0.1 Intermediate; ACAud/1.0; BAA/1.0; CAA/1.0; CASLPA/1.0; IHS/1.0; Kansas DHE, LTS-S0035/1.0 Cost: Free to View Join the senior audiology staff and their students at Henry Ford Hospital in Detroit, Michigan as they highlight interesting clinical cases in a grand rounds style format. In addition to the case presentations, a live video feed will capture spontaneous questions, discussion and debate that make the department’s staff meetings lively, insightful and thought-provoking in order to facilitate clinical decision-making and best practices. This session will cover vestibular cases. For information and to register for other courses in this series please visit www.audiologyonline.com/grandrounds Course Details Presenter Gayle E. Hicks, PhD, CCC-A, DABNM Intra-operative Neurologic Monitoring as a Career Path for Audiologists [Recorded Course] Course: #20048 CEUs/Hours Offered: AAA/0.2 Intermediate; ACAud/0.2; ASHA/0.2 Intermediate, Professional; BAA/2.0; CAA/2.0; CASLPA/2.0; IHS/2.0; Kansas DHE, LTS-S0035/2.0 Cost: Free to View The purpose of this presentation is to offer information on the field of intra-operative monitoring for the audiologist considering it as a potential career path. The presentation will introduce the OR environment, demonstrate the manner of clinical application of electrophysiology during surgery, and qualifications necessary to perform neuro-physiological intra-operative monitoring. Course Details
